Chambery's disease is a fairly common pathology of a chronic nature, which occurs due to the defeat of skin capillaries. As a result, point hemorrhages appear, resembling the consequences of an injection with the most common needle.
Disease Description
Chambery's disease (skin hemosiderosis, chronic pigmented purpura) is a pathology characterized by damage to the vessels of the skin, in which the normal permeability of the capillaries changes, numerous point hemorrhages occur. Diagnosis is based on the results of dermatoscopy. Further therapy involves the use of anti-inflammatory drugs, glucocorticoids. All drugs are prescribed on an individual basis and only after the doctor confirms Schamberg's disease.
The causes of this pathology are not fully understood. It is believed that autoimmune changes underlie capillary damage. This pathological process is associated with the sequential deposition of circulating immune complexes on their walls. Due to inflammation, the permeability of various areas of the walls of the capillaries increases, which entails the appearance of intradermal petechial hemorrhages. Over time, the iron contained in hemoglobin is transformed into the pigment hemosiderin, which explains the brown tint of the spots in this disease.
Main reasons
Chambery's disease begins to manifest itself with external signs when the walls of the vessels allow red blood cells to penetrate the skin. Then these cells are deformed and "release" the iron. As a result, a brownish shading of the lesions is observed. Although the main reason for such vascular leakage remains unknown, specialists were able to identify several factors that provoke the disease (viral infections, hypersensitivity to certain drugs).
Cases of transmission of the disease over several generations in the same family are also known. This makes it possible to assume the presence of a special genetic factor that precedes the disease.
Many researchers consider the disease to be autoimmune. This means that the body itself is gradually destroying the components of the vascular wall, but strictly defined.
Pathology can occur at absolutely any age, regardless of human race. Note, Schamberg's disease in women is diagnosed several times less than in men.
Clinical picture
- Symmetric rashes on the skin. Initially, point hemorrhages occur. Combining, they form yellow plaques that, over time, acquire a brown hue. At the edges of these plaques, new bright red rashes are formed, about the size of a pinhead. Later, the central region becomes thinner and begins to atrophy.
- Rashes are localized mainly in the hips, on the legs, rarely on the trunk and arms. Some patients report itching.
- In some cases, changes in the functioning of the circulatory system are diagnosed (for example, a decrease in the number of red blood cells).
Classification
Chambert's disease is classified into four types. Each of them is described in more detail below.
- Petechial. It is diagnosed mainly in men. Rashes are localized in the shins and thighs. They are spots of different diameters with an uneven brown outline.
- Lichenoid. This type of disease is characterized by the appearance of a rash throughout the body and nodules on the skin. Sometimes point hemorrhages form.
- Teleangiectatic. The rash appears in the form of medallion spots. In the center, deformed subcutaneous vessels are localized, and at the edges - the smallest point hemorrhages. Rashes do not cause discomfort.
- Eczematous. Affected areas are characterized by increased swelling. At the site of rashes, after a few days, bubbles with crusts appear. Patients usually complain of severe itching.
Diagnostics
Today, many people are able to independently diagnose themselves with "Chamberberg's disease." A photo of the characteristic clinical picture with this pathology can be found in medical directories. However, do not neglect qualified help for two reasons. Firstly, if you suspect this disease, differential diagnosis with other ailments is always required (varicose dermatitis, Bateman senile purpura, etc.). It is often difficult even to distinguish one disease from another. Secondly, competent medical treatment can slow the progression of the disease.
It is important to note that the initial diagnosis is determined based on the typical symptoms of the disease (rash, pruritus). Then a number of laboratory tests are prescribed, including a blood test, biopsy, and dermatoscopy.
What should be the treatment?
Therapy is prescribed strictly individually and after the specialist confirms Schamberg's disease. Treatment involves taking angioprotectors to strengthen the walls of blood vessels (Diosmin, Hesperidin). The standard course of therapy lasts at least two months. To reduce the inflammatory process and pain, non-steroidal anti-inflammatory drugs and corticosteroids (Prednisolone) are prescribed.
An eczematous variant of the disease involves taking antihistamines (Cetirizine). To restore blood parameters with a clear loss of hemoglobin, iron preparations are usually recommended for patients . They are responsible for the natural stimulation of hematopoietic bone marrow sprouts.
With this disease, the prognosis is generally favorable. Schamberg's disease (photos can be viewed in this article) does not affect a person’s well-being. Of course, its external manifestation in the form of rashes on the skin can significantly reduce the quality of life, because in this case a person is literally forced to refuse to open clothes, shy of his appearance.
ethnoscience
How else can I overcome Chamberlain's disease? Treatment with folk remedies is not an alternative to conservative therapy. It is recommended to resort to his help as an additional method of combating pathology.
- Decoction of thick frankincense. You will need to take 50 mg of the frankincense herb and pour 250 ml of water, boil until half the volume of liquid is boiled. Such a medicine should be taken 20 drops three times a day.
- Mountain arnica, coupled with hazel bark, is great for strengthening the vascular network. These plant components will need to be taken in equal proportions and pour boiling water (0.5 l per tablespoon of dry mix). The resulting infusion must be kept in a dark place for 12 hours, and then taken before meals, one tablespoon.
Such simple recipes can slow down Schamberg's disease, the symptoms of which often prevent a person from leading a normal lifestyle, violating its quality.
General recommendations
All patients who have encountered such an unpleasant pathology, doctors are advised to follow a certain diet. It implies a rejection of fried and smoked products, citrus fruits, chocolate, coffee, alcohol. In a word, it is necessary to completely exclude all allergenic foods from the diet.
To reduce the load on the superficial vessels of the legs, it is recommended to avoid bruises, hypothermia. It is extremely important to carefully care for the skin, use exclusively hypoallergenic cosmetics. Much attention must be paid to the timely rehabilitation of foci of infection and the treatment of concomitant diseases. The latter often play the role of a supporting factor in Schamberg's disease.